E75 Disorders of sphingolipid metabolism and other lipid storage disorders

Category / Non-billable header 30 subcodes

Block: Metabolic disorders (E70-E88)

Excludes 1 (cannot be coded together)

  • mucolipidosis, types I-III (E77.0-E77.1)
  • Refsum's disease (G60.1)

Subcodes

Each subcode links to a detail page with full clinical annotations.

Code Description Billable
E75..0 GM2 gangliosidosis No
E75..00 GM2 gangliosidosis, unspecified Yes
E75..01 Sandhoff disease Yes
E75..02 Tay-Sachs disease Yes
E75..09 Other GM2 gangliosidosis Yes
E75..1 Other and unspecified gangliosidosis No
E75..10 Unspecified gangliosidosis Yes
E75..11 Mucolipidosis IV Yes
E75..19 Other gangliosidosis Yes
E75..2 Other sphingolipidosis No
E75..21 Fabry (-Anderson) disease Yes
E75..22 Gaucher disease Yes
E75..23 Krabbe disease Yes
E75..24 Niemann-Pick disease No
E75..240 Niemann-Pick disease type A Yes
E75..241 Niemann-Pick disease type B Yes
E75..242 Niemann-Pick disease type C Yes
E75..243 Niemann-Pick disease type D Yes
E75..244 Niemann-Pick disease type A/B Yes
E75..248 Other Niemann-Pick disease Yes
E75..249 Niemann-Pick disease, unspecified Yes
E75..25 Metachromatic leukodystrophy Yes
E75..26 Sulfatase deficiency Yes
E75..27 Pelizaeus-Merzbacher disease Yes
E75..28 Canavan disease Yes
E75..29 Other sphingolipidosis Yes
E75..3 Sphingolipidosis, unspecified Yes
E75..4 Neuronal ceroid lipofuscinosis Yes
E75..5 Other lipid storage disorders Yes
E75..6 Lipid storage disorder, unspecified Yes

Last reviewed: September 2026