ICD-10-CM · Chapter 4 · E00-E89
E76 Disorders of glycosaminoglycan metabolism
Subcodes
Each subcode links to a detail page with full clinical annotations.
| Code | Description | Billable |
|---|---|---|
| E76..0 | Mucopolysaccharidosis, type I | No |
| E76..01 | Hurler's syndrome | Yes |
| E76..02 | Hurler-Scheie syndrome | Yes |
| E76..03 | Scheie's syndrome | Yes |
| E76..1 | Mucopolysaccharidosis, type II | Yes |
| E76..2 | Other mucopolysaccharidoses | No |
| E76..21 | Morquio mucopolysaccharidoses | No |
| E76..210 | Morquio A mucopolysaccharidoses | Yes |
| E76..211 | Morquio B mucopolysaccharidoses | Yes |
| E76..219 | Morquio mucopolysaccharidoses, unspecified | Yes |
| E76..22 | Sanfilippo mucopolysaccharidoses | Yes |
| E76..29 | Other mucopolysaccharidoses | Yes |
| E76..3 | Mucopolysaccharidosis, unspecified | Yes |
| E76..8 | Other disorders of glucosaminoglycan metabolism | Yes |
| E76..9 | Glucosaminoglycan metabolism disorder, unspecified | Yes |
Last reviewed: September 2026