ICD-10-CM · Chapter 4

E75..241 Niemann-Pick disease type B

Billable

← E75 — Disorders of sphingolipid metabolism and other lipid storage disorders Chapter 4: E00-E89

Includes

Acid sphingomyelinase deficiency type B (ASMD type B)
Chronic visceral acid sphingomyelinase deficiency

Last reviewed: September 2026