ICD-10-CM · Chapter 4 · E00-E89
E78 Disorders of lipoprotein metabolism and other lipidemias
Excludes 1 (cannot be coded together)
- sphingolipidosis (E75.0-E75.3)
Subcodes
Each subcode links to a detail page with full clinical annotations.
| Code | Description | Billable |
|---|---|---|
| E78..0 | Pure hypercholesterolemia | No |
| E78..00 | Pure hypercholesterolemia, unspecified | Yes |
| E78..01 | Familial hypercholesterolemia | No |
| E78..010 | Homozygous familial hypercholesterolemia [HoFH] | Yes |
| E78..011 | Heterozygous familial hypercholesterolemia [HeFH] | Yes |
| E78..019 | Familial hypercholesterolemia, unspecified | Yes |
| E78..1 | Pure hyperglyceridemia | Yes |
| E78..2 | Mixed hyperlipidemia | Yes |
| E78..3 | Hyperchylomicronemia | Yes |
| E78..4 | Other hyperlipidemia | No |
| E78..41 | Elevated Lipoprotein(a) | Yes |
| E78..49 | Other hyperlipidemia | Yes |
| E78..5 | Hyperlipidemia, unspecified | Yes |
| E78..6 | Lipoprotein deficiency | Yes |
| E78..7 | Disorders of bile acid and cholesterol metabolism | No |
| E78..70 | Disorder of bile acid and cholesterol metabolism, unspecified | Yes |
| E78..71 | Barth syndrome | Yes |
| E78..72 | Smith-Lemli-Opitz syndrome | Yes |
| E78..79 | Other disorders of bile acid and cholesterol metabolism | Yes |
| E78..8 | Other disorders of lipoprotein metabolism | No |
| E78..81 | Lipoid dermatoarthritis | Yes |
| E78..89 | Other lipoprotein metabolism disorders | Yes |
| E78..9 | Disorder of lipoprotein metabolism, unspecified | Yes |
Plain-language term for this code
The following entry in the US Medical Glossary corresponds to ICD-10-CM category E78:
- Hyperlipidemia — Hiperlipidemia
Last reviewed: September 2026