ICD-10-CM · Chapter 4

E75..240 Niemann-Pick disease type A

Billable

← E75 — Disorders of sphingolipid metabolism and other lipid storage disorders Chapter 4: E00-E89

Includes

Acid sphingomyelinase deficiency type A (ASMD type A)
Infantile neurovisceral acid sphingomyelinase deficiency

Last reviewed: September 2026