ICD-10-CM · Chapter 4 · E00-E89
E74 Other disorders of carbohydrate metabolism
Excludes 1 (cannot be coded together)
- diabetes mellitus (E08-E13)
- hypoglycemia NOS (E16.2)
- increased secretion of glucagon (E16.3)
- mucopolysaccharidosis (E76.0-E76.3)
Subcodes
Each subcode links to a detail page with full clinical annotations.
| Code | Description | Billable |
|---|---|---|
| E74..0 | Glycogen storage disease | No |
| E74..00 | Glycogen storage disease, unspecified | Yes |
| E74..01 | von Gierke disease | Yes |
| E74..02 | Pompe disease | Yes |
| E74..03 | Cori disease | Yes |
| E74..04 | McArdle disease | Yes |
| E74..05 | Lysosome-associated membrane protein 2 [LAMP2] deficiency | Yes |
| E74..09 | Other glycogen storage disease | Yes |
| E74..1 | Disorders of fructose metabolism | No |
| E74..10 | Disorder of fructose metabolism, unspecified | Yes |
| E74..11 | Essential fructosuria | Yes |
| E74..12 | Hereditary fructose intolerance | Yes |
| E74..19 | Other disorders of fructose metabolism | Yes |
| E74..2 | Disorders of galactose metabolism | No |
| E74..20 | Disorders of galactose metabolism, unspecified | Yes |
| E74..21 | Galactosemia | Yes |
| E74..29 | Other disorders of galactose metabolism | Yes |
| E74..3 | Other disorders of intestinal carbohydrate absorption | No |
| E74..31 | Sucrase-isomaltase deficiency | Yes |
| E74..39 | Other disorders of intestinal carbohydrate absorption | Yes |
| E74..4 | Disorders of pyruvate metabolism and gluconeogenesis | Yes |
| E74..8 | Other specified disorders of carbohydrate metabolism | No |
| E74..81 | Disorders of glucose transport, not elsewhere classified | No |
| E74..810 | Glucose transporter protein type 1 deficiency | Yes |
| E74..818 | Other disorders of glucose transport | Yes |
| E74..819 | Disorders of glucose transport, unspecified | Yes |
| E74..82 | Disorders of citrate metabolism | No |
| E74..820 | SLC13A5 Citrate Transporter Disorder | Yes |
| E74..829 | Other disorders of citrate metabolism | Yes |
| E74..89 | Other specified disorders of carbohydrate metabolism | Yes |
| E74..9 | Disorder of carbohydrate metabolism, unspecified | Yes |
Last reviewed: September 2026