ICD-10-CM · Chapter 4

E74..4 Disorders of pyruvate metabolism and gluconeogenesis

Billable

← E74 — Other disorders of carbohydrate metabolism Chapter 4: E00-E89

Includes

Deficiency of phosphoenolpyruvate carboxykinase
Deficiency of pyruvate carboxylase
Deficiency of pyruvate dehydrogenase

Excludes 1 (cannot be coded together)

disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
Leigh's syndrome (G31.82)

Last reviewed: September 2026