ICD-10-CM · Chapter 4
E88..43 Disorders of mitochondrial tRNA synthetases
Includes
- ARS2-related mitochondrial disorders
- LBSL
- Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation
- Leukoencephalopathy with thalamus - brainstem involvement - high lactate
- LTBL
- Mitochondrial aminoacyl-tRNA synthetase disorders
Code Also
- , if applicable, associated condition such as:
- leukoencephalopathy (G93.49)
Last reviewed: September 2026