ICD-10-CM · Chapter 4
E88..4 Mitochondrial metabolism disorders
Excludes 1 (cannot be coded together)
- disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)
Last reviewed: September 2026