J84..178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

Billable

Includes

  • Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
  • Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
  • Organizing pneumonia due to collagen vascular disease
  • Organizing pneumonia in diseases classified elsewhere

Code First

  • underlying disease, such as:
  • progressive systemic sclerosis (M34.0)
  • rheumatoid arthritis (M05.00-M06.9)
  • systemic lupus erythematosis (M32.0-M32.9)

Last reviewed: September 2026