ICD-10-CM · Chapter 10 · J00-J99
J84 Other interstitial pulmonary diseases
Excludes 1 (cannot be coded together)
- drug-induced interstitial lung disorders (J70.2-J70.4)
- interstitial emphysema (J98.2)
Excludes 2 (not included here)
- lung diseases due to external agents (J60-J70)
Code Also
- , if applicable, associated condition
Subcodes
Each subcode links to a detail page with full clinical annotations.
| Code | Description | Billable |
|---|---|---|
| J84..0 | Alveolar and parieto-alveolar conditions | No |
| J84..01 | Alveolar proteinosis | Yes |
| J84..02 | Pulmonary alveolar microlithiasis | Yes |
| J84..03 | Idiopathic pulmonary hemosiderosis | Yes |
| J84..09 | Other alveolar and parieto-alveolar conditions | Yes |
| J84..1 | Other interstitial pulmonary diseases with fibrosis | No |
| J84..10 | Pulmonary fibrosis, unspecified | Yes |
| J84..11 | Idiopathic interstitial pneumonia | No |
| J84..111 | Idiopathic interstitial pneumonia, not otherwise specified | Yes |
| J84..112 | Idiopathic pulmonary fibrosis | Yes |
| J84..113 | Idiopathic non-specific interstitial pneumonitis | Yes |
| J84..114 | Acute interstitial pneumonitis | Yes |
| J84..115 | Respiratory bronchiolitis interstitial lung disease | Yes |
| J84..116 | Cryptogenic organizing pneumonia | Yes |
| J84..117 | Desquamative interstitial pneumonia | Yes |
| J84..17 | Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere | No |
| J84..170 | Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere | Yes |
| J84..178 | Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere | Yes |
| J84..2 | Lymphoid interstitial pneumonia | Yes |
| J84..8 | Other specified interstitial pulmonary diseases | No |
| J84..81 | Lymphangioleiomyomatosis | Yes |
| J84..82 | Adult pulmonary Langerhans cell histiocytosis | Yes |
| J84..83 | Surfactant mutations of the lung | Yes |
| J84..84 | Other interstitial lung diseases of childhood | No |
| J84..841 | Neuroendocrine cell hyperplasia of infancy | Yes |
| J84..842 | Pulmonary interstitial glycogenosis | Yes |
| J84..843 | Alveolar capillary dysplasia with vein misalignment | Yes |
| J84..848 | Other interstitial lung diseases of childhood | Yes |
| J84..89 | Other specified interstitial pulmonary diseases | Yes |
| J84..9 | Interstitial pulmonary disease, unspecified | Yes |
Plain-language term for this code
The following entry in the US Medical Glossary corresponds to ICD-10-CM category J84:
- Pulmonary Fibrosis — Fibrosis pulmonar
Last reviewed: September 2026