ICD-10-CM · Chapter 6
G71..3 Mitochondrial myopathy, not elsewhere classified
Excludes 1 (cannot be coded together)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.21)
- Leigh's encephalopathy (G31.82)
- mitochondrial metabolism disorders (E88.4.-)
- Reye's syndrome (G93.7)
Last reviewed: September 2026