G71 Primary disorders of muscles

Category / Non-billable header 34 subcodes

Block: Diseases of myoneural junction and muscle (G70-G73)

Excludes 2 (not included here)

  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)

Subcodes

Each subcode links to a detail page with full clinical annotations.

Code Description Billable
G71..0 Muscular dystrophy No
G71..00 Muscular dystrophy, unspecified Yes
G71..01 Duchenne or Becker muscular dystrophy Yes
G71..02 Facioscapulohumeral muscular dystrophy Yes
G71..03 Limb girdle muscular dystrophies No
G71..031 Autosomal dominant limb girdle muscular dystrophy Yes
G71..032 Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction Yes
G71..033 Limb girdle muscular dystrophy due to dysferlin dysfunction Yes
G71..034 Limb girdle muscular dystrophy due to sarcoglycan dysfunction No
G71..0340 Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified Yes
G71..0341 Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction Yes
G71..0342 Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction Yes
G71..0349 Limb girdle muscular dystrophy due to other sarcoglycan dysfunction Yes
G71..035 Limb girdle muscular dystrophy due to anoctamin-5 dysfunction Yes
G71..036 Limb girdle muscular dystrophy due to fukutin related protein dysfunction Yes
G71..038 Other limb girdle muscular dystrophy Yes
G71..039 Limb girdle muscular dystrophy, unspecified Yes
G71..09 Other specified muscular dystrophies Yes
G71..1 Myotonic disorders No
G71..11 Myotonic muscular dystrophy Yes
G71..12 Myotonia congenita Yes
G71..13 Myotonic chondrodystrophy Yes
G71..14 Drug induced myotonia Yes
G71..19 Other specified myotonic disorders Yes
G71..2 Congenital myopathies No
G71..20 Congenital myopathy, unspecified Yes
G71..21 Nemaline myopathy Yes
G71..22 Centronuclear myopathy No
G71..220 X-linked myotubular myopathy Yes
G71..228 Other centronuclear myopathy Yes
G71..29 Other congenital myopathy Yes
G71..3 Mitochondrial myopathy, not elsewhere classified Yes
G71..8 Other primary disorders of muscles Yes
G71..9 Primary disorder of muscle, unspecified Yes

Last reviewed: September 2026