N00 Acute nephritic syndrome

Category / Non-billable header 14 subcodes

Block: Glomerular diseases (N00-N08)

Includes

  • acute glomerular disease
  • acute glomerulonephritis
  • acute nephritis

Excludes 1 (cannot be coded together)

  • acute tubulo-interstitial nephritis (N10)
  • nephritic syndrome NOS (N05.-)

Subcodes

Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.

Code Description Billable
N00..0 Acute nephritic syndrome with minor glomerular abnormality Yes
N00..1 Acute nephritic syndrome with focal and segmental glomerular lesions Yes
N00..2 Acute nephritic syndrome with diffuse membranous glomerulonephritis Yes
N00..3 Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis Yes
N00..4 Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis Yes
N00..5 Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis Yes
N00..6 Acute nephritic syndrome with dense deposit disease Yes
N00..7 Acute nephritic syndrome with diffuse crescentic glomerulonephritis Yes
N00..8 Acute nephritic syndrome with other morphologic changes Yes
N00..9 Acute nephritic syndrome with unspecified morphologic changes Yes
N00..A Acute nephritic syndrome with C3 glomerulonephritis Yes
N00..B Acute nephritic syndrome with immune complex membranoproliferative glomerulonephritis No
N00..B1 Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN) Yes
N00..B2 Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN) Yes

Last reviewed: September 2026