N01 Rapidly progressive nephritic syndrome

Category / Non-billable header 11 subcodes

Block: Glomerular diseases (N00-N08)

Includes

  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Excludes 1 (cannot be coded together)

  • nephritic syndrome NOS (N05.-)

Subcodes

Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.

Code Description Billable
N01..0 Rapidly progressive nephritic syndrome with minor glomerular abnormality Yes
N01..1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions Yes
N01..2 Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis Yes
N01..3 Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis Yes
N01..4 Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis Yes
N01..5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis Yes
N01..6 Rapidly progressive nephritic syndrome with dense deposit disease Yes
N01..7 Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis Yes
N01..8 Rapidly progressive nephritic syndrome with other morphologic changes Yes
N01..9 Rapidly progressive nephritic syndrome with unspecified morphologic changes Yes
N01..A Rapidly progressive nephritic syndrome with C3 glomerulonephritis Yes

Last reviewed: September 2026