D57 Sickle-cell disorders

Category / Non-billable header 52 subcodes

Block: Hemolytic anemias (D55-D59)

Excludes 1 (cannot be coded together)

  • other hemoglobinopathies (D58.-)

Use Additional Code

  • code for any associated fever (R50.81)

Subcodes

Each subcode links to a detail page with full clinical annotations.

Code Description Billable
D57..0 Hb-SS disease with crisis No
D57..00 Hb-SS disease with crisis, unspecified Yes
D57..01 Hb-SS disease with acute chest syndrome Yes
D57..02 Hb-SS disease with splenic sequestration Yes
D57..03 Hb-SS disease with cerebral vascular involvement Yes
D57..04 Hb-SS disease with dactylitis Yes
D57..09 Hb-SS disease with crisis with other specified complication Yes
D57..1 Sickle-cell disease without crisis Yes
D57..2 Sickle-cell/Hb-C disease No
D57..20 Sickle-cell/Hb-C disease without crisis Yes
D57..21 Sickle-cell/Hb-C disease with crisis No
D57..211 Sickle-cell/Hb-C disease with acute chest syndrome Yes
D57..212 Sickle-cell/Hb-C disease with splenic sequestration Yes
D57..213 Sickle-cell/Hb-C disease with cerebral vascular involvement Yes
D57..214 Sickle-cell/Hb-C disease with dactylitis Yes
D57..218 Sickle-cell/Hb-C disease with crisis with other specified complication Yes
D57..219 Sickle-cell/Hb-C disease with crisis, unspecified Yes
D57..3 Sickle-cell trait Yes
D57..4 Sickle-cell thalassemia No
D57..40 Sickle-cell thalassemia without crisis Yes
D57..41 Sickle-cell thalassemia, unspecified, with crisis No
D57..411 Sickle-cell thalassemia, unspecified, with acute chest syndrome Yes
D57..412 Sickle-cell thalassemia, unspecified, with splenic sequestration Yes
D57..413 Sickle-cell thalassemia, unspecified, with cerebral vascular involvement Yes
D57..414 Sickle-cell thalassemia, unspecified, with dactylitis Yes
D57..418 Sickle-cell thalassemia, unspecified, with crisis with other specified complication Yes
D57..419 Sickle-cell thalassemia, unspecified, with crisis Yes
D57..42 Sickle-cell thalassemia beta zero without crisis Yes
D57..43 Sickle-cell thalassemia beta zero with crisis No
D57..431 Sickle-cell thalassemia beta zero with acute chest syndrome Yes
D57..432 Sickle-cell thalassemia beta zero with splenic sequestration Yes
D57..433 Sickle-cell thalassemia beta zero with cerebral vascular involvement Yes
D57..434 Sickle-cell thalassemia beta zero with dactylitis Yes
D57..438 Sickle-cell thalassemia beta zero with crisis with other specified complication Yes
D57..439 Sickle-cell thalassemia beta zero with crisis, unspecified Yes
D57..44 Sickle-cell thalassemia beta plus without crisis Yes
D57..45 Sickle-cell thalassemia beta plus with crisis No
D57..451 Sickle-cell thalassemia beta plus with acute chest syndrome Yes
D57..452 Sickle-cell thalassemia beta plus with splenic sequestration Yes
D57..453 Sickle-cell thalassemia beta plus with cerebral vascular involvement Yes
D57..454 Sickle-cell thalassemia beta plus with dactylitis Yes
D57..458 Sickle-cell thalassemia beta plus with crisis with other specified complication Yes
D57..459 Sickle-cell thalassemia beta plus with crisis, unspecified Yes
D57..8 Other sickle-cell disorders No
D57..80 Other sickle-cell disorders without crisis Yes
D57..81 Other sickle-cell disorders with crisis No
D57..811 Other sickle-cell disorders with acute chest syndrome Yes
D57..812 Other sickle-cell disorders with splenic sequestration Yes
D57..813 Other sickle-cell disorders with cerebral vascular involvement Yes
D57..814 Other sickle-cell disorders with dactylitis Yes
D57..818 Other sickle-cell disorders with crisis with other specified complication Yes
D57..819 Other sickle-cell disorders with crisis, unspecified Yes

Last reviewed: September 2026