D55 Anemia due to enzyme disorders

Category / Non-billable header 8 subcodes

Block: Hemolytic anemias (D55-D59)

Excludes 1 (cannot be coded together)

  • drug-induced enzyme deficiency anemia (D59.2)

Subcodes

Each subcode links to a detail page with full clinical annotations.

Code Description Billable
D55..0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency Yes
D55..1 Anemia due to other disorders of glutathione metabolism Yes
D55..2 Anemia due to disorders of glycolytic enzymes No
D55..21 Anemia due to pyruvate kinase deficiency Yes
D55..29 Anemia due to other disorders of glycolytic enzymes Yes
D55..3 Anemia due to disorders of nucleotide metabolism Yes
D55..8 Other anemias due to enzyme disorders Yes
D55..9 Anemia due to enzyme disorder, unspecified Yes

Last reviewed: September 2026