ICD-10-CM · Chapter 17 · Q00-QA1
Q85 Phakomatoses, not elsewhere classified
Excludes 1 (cannot be coded together)
- ataxia telangiectasia [Louis-Bar] (G11.3)
- familial dysautonomia [Riley-Day] (G90.1)
Subcodes
Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.
| Code | Description | Billable |
|---|---|---|
| Q85..0 | Neurofibromatosis (nonmalignant) | No |
| Q85..00 | Neurofibromatosis, unspecified | Yes |
| Q85..01 | Neurofibromatosis, type 1 | Yes |
| Q85..02 | Neurofibromatosis, type 2 | Yes |
| Q85..03 | Schwannomatosis | Yes |
| Q85..09 | Other neurofibromatosis | Yes |
| Q85..1 | Tuberous sclerosis | Yes |
| Q85..8 | Other phakomatoses, not elsewhere classified | No |
| Q85..81 | PTEN hamartoma tumor syndrome | Yes |
| Q85..82 | Other Cowden syndrome | Yes |
| Q85..83 | Von Hippel-Lindau syndrome | Yes |
| Q85..89 | Other phakomatoses, not elsewhere classified | Yes |
| Q85..9 | Phakomatosis, unspecified | Yes |
Last reviewed: September 2026