ICD-10-CM · Chapter 17 · Q00-QA1
Q87 Other specified congenital malformation syndromes affecting multiple systems
Use Additional Code
- code(s) to identify all associated manifestations
Subcodes
Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.
| Code | Description | Billable |
|---|---|---|
| Q87..0 | Congenital malformation syndromes predominantly affecting facial appearance | Yes |
| Q87..1 | Congenital malformation syndromes predominantly associated with short stature | No |
| Q87..11 | Prader-Willi syndrome | Yes |
| Q87..19 | Other congenital malformation syndromes predominantly associated with short stature | Yes |
| Q87..2 | Congenital malformation syndromes predominantly involving limbs | Yes |
| Q87..3 | Congenital malformation syndromes involving early overgrowth | Yes |
| Q87..4 | Marfan syndrome | No |
| Q87..40 | Marfan syndrome, unspecified | Yes |
| Q87..41 | Marfan syndrome with cardiovascular manifestations | No |
| Q87..410 | Marfan syndrome with aortic dilation | Yes |
| Q87..418 | Marfan syndrome with other cardiovascular manifestations | Yes |
| Q87..42 | Marfan syndrome with ocular manifestations | Yes |
| Q87..43 | Marfan syndrome with skeletal manifestation | Yes |
| Q87..5 | Other congenital malformation syndromes with other skeletal changes | Yes |
| Q87..8 | Other specified congenital malformation syndromes, not elsewhere classified | No |
| Q87..81 | Alport syndrome | Yes |
| Q87..82 | Arterial tortuosity syndrome | Yes |
| Q87..83 | Bardet-Biedl syndrome | Yes |
| Q87..84 | Laurence-Moon syndrome | Yes |
| Q87..85 | MED13L syndrome | Yes |
| Q87..86 | Kleefstra syndrome | Yes |
| Q87..87 | Hao-Fountain Syndrome | Yes |
| Q87..88 | CTNNB1 syndrome | Yes |
| Q87..89 | Other specified congenital malformation syndromes, not elsewhere classified | Yes |
| Q87..A | Loeys-Dietz syndrome | Yes |
Last reviewed: September 2026