Q05 Spina bifida

Category / Non-billable header 10 subcodes

Block: Congenital malformations of the nervous system (Q00-Q07)

Includes

  • hydromeningocele (spinal)
  • meningocele (spinal)
  • meningomyelocele
  • myelocele
  • myelomeningocele
  • rachischisis
  • spina bifida (aperta)(cystica)
  • syringomyelocele

Excludes 1 (cannot be coded together)

  • Arnold-Chiari syndrome, type II (Q07.0-)
  • spina bifida occulta (Q76.0)

Use Additional Code

  • code for any associated paraplegia (paraparesis) (G82.2-)

Subcodes

Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.

Code Description Billable
Q05..0 Cervical spina bifida with hydrocephalus Yes
Q05..1 Thoracic spina bifida with hydrocephalus Yes
Q05..2 Lumbar spina bifida with hydrocephalus Yes
Q05..3 Sacral spina bifida with hydrocephalus Yes
Q05..4 Unspecified spina bifida with hydrocephalus Yes
Q05..5 Cervical spina bifida without hydrocephalus Yes
Q05..6 Thoracic spina bifida without hydrocephalus Yes
Q05..7 Lumbar spina bifida without hydrocephalus Yes
Q05..8 Sacral spina bifida without hydrocephalus Yes
Q05..9 Spina bifida, unspecified Yes

Last reviewed: September 2026