Emergency: 119
AMDA-IMIC

D47..02 Systemic mastocytosis

Billable

← D47 — Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue Chapter 2: C00-D49

Includes

  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)

Excludes 1 (cannot be coded together)

  • aggressive systemic mastocytosis (C96.21)
  • mast cell leukemia (C94.3-)

Code Also

  • , if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (C92.6-, C92.A-)
  • chronic myelomonocytic leukemia (C93.1-)
  • essential thrombocytosis (D47.3)
  • hypereosinophilic syndrome (D72.1)
  • myelodysplastic syndrome (D46.9)
  • myeloproliferative syndrome (D47.1)
  • non-Hodgkin lymphoma (C82-C85)
  • plasma cell myeloma (C90.0-)
  • polycythemia vera (D45)

Last reviewed: September 2026