ICD-10-CM · Chapter 2
D47..01 Cutaneous mastocytosis
← D47 — Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
Chapter 2: C00-D49
Includes
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Excludes 1 (cannot be coded together)
- congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- congenital urticaria pigmentosa (Q82.2)
- extracutaneous mastocytoma (D47.09)
Last reviewed: September 2026