ICD-10-CM · Chapter 4
E71..51 Disorders of peroxisome biogenesis
← E71 — Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Chapter 4: E00-E89
Includes
- Group 1 peroxisomal disorders
Excludes 1 (cannot be coded together)
- Refsum's disease (G60.1)
Last reviewed: September 2026