E27..1 Primary adrenocortical insufficiency

Billable

Includes

  • Addison's disease
  • Autoimmune adrenalitis

Excludes 1 (cannot be coded together)

  • Addison only phenotype adrenoleukodystrophy (E71.528)
  • amyloidosis (E85.-)
  • tuberculous Addison's disease (A18.7)
  • Waterhouse-Friderichsen syndrome (A39.1)

Last reviewed: September 2026