J99 Respiratory disorders in diseases classified elsewhere

Billable

Block: Other diseases of the respiratory system (J96-J99)

Excludes 1 (cannot be coded together)

  • respiratory disorders in:
  • amebiasis (A06.5)
  • blastomycosis (B40.0-B40.2)
  • candidiasis (B37.1)
  • coccidioidomycosis (B38.0-B38.2)
  • cystic fibrosis with pulmonary manifestations (E84.0)
  • dermatomyositis (M33.01, M33.11)
  • histoplasmosis (B39.0-B39.2)
  • late syphilis (A52.72, A52.73)
  • polymyositis (M33.21)
  • Sjögren syndrome (M35.02)
  • systemic lupus erythematosus (M32.13)
  • systemic sclerosis (M34.81)
  • Wegener's granulomatosis (M31.30-M31.31)

Code First

  • underlying disease, such as:
  • amyloidosis (E85.-)
  • ankylosing spondylitis (M45.-)
  • bronchomycosis (B49)
  • congenital syphilis (A50.-)
  • cryoglobulinemia (D89.1)
  • early congenital syphilis (A50.0-)
  • plasminogen deficiency (E88.02)
  • schistosomiasis (B65.0-B65.9)
This category is a complete, billable diagnosis code.

No additional specificity is required — submit J99 directly on claims and documentation without a subcode extension.

Last reviewed: September 2026