G04 Encephalitis, myelitis and encephalomyelitis

Category / Non-billable header 18 subcodes

Block: Inflammatory diseases of the central nervous system (G00-G09)

Includes

  • acute ascending myelitis
  • meningoencephalitis
  • meningomyelitis

Excludes 1 (cannot be coded together)

  • encephalopathy NOS (G93.40)

Excludes 2 (not included here)

  • acute transverse myelitis (G37.3)
  • alcoholic encephalopathy (G31.2)
  • multiple sclerosis (G35-)
  • myalgic encephalomyelitis (G93.32)
  • subacute necrotizing myelitis (G37.4)
  • toxic encephalitis (G92.8)
  • toxic encephalopathy (G92.8)

Subcodes

Each subcode links to a detail page with full clinical annotations.

Code Description Billable
G04..0 Acute disseminated encephalitis and encephalomyelitis (ADEM) No
G04..00 Acute disseminated encephalitis and encephalomyelitis, unspecified Yes
G04..01 Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM) Yes
G04..02 Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis Yes
G04..1 Tropical spastic paraplegia Yes
G04..2 Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified Yes
G04..3 Acute necrotizing hemorrhagic encephalopathy No
G04..30 Acute necrotizing hemorrhagic encephalopathy, unspecified Yes
G04..31 Postinfectious acute necrotizing hemorrhagic encephalopathy Yes
G04..32 Postimmunization acute necrotizing hemorrhagic encephalopathy Yes
G04..39 Other acute necrotizing hemorrhagic encephalopathy Yes
G04..8 Other encephalitis, myelitis and encephalomyelitis No
G04..81 Other encephalitis and encephalomyelitis Yes
G04..82 Acute flaccid myelitis Yes
G04..89 Other myelitis Yes
G04..9 Encephalitis, myelitis and encephalomyelitis, unspecified No
G04..90 Encephalitis and encephalomyelitis, unspecified Yes
G04..91 Myelitis, unspecified Yes

Last reviewed: September 2026