M34 Systemic sclerosis [scleroderma]

Category / Non-billable header 9 subcodes

Block: Systemic connective tissue disorders (M30-M36)

Excludes 1 (cannot be coded together)

  • circumscribed scleroderma (L94.0)
  • neonatal scleroderma (P83.88)

Subcodes

Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.

Code Description Billable
M34..0 Progressive systemic sclerosis Yes
M34..1 CR(E)ST syndrome Yes
M34..2 Systemic sclerosis induced by drug and chemical Yes
M34..8 Other forms of systemic sclerosis No
M34..81 Systemic sclerosis with lung involvement Yes
M34..82 Systemic sclerosis with myopathy Yes
M34..83 Systemic sclerosis with polyneuropathy Yes
M34..89 Other systemic sclerosis Yes
M34..9 Systemic sclerosis, unspecified Yes

Last reviewed: September 2026