M04 Autoinflammatory syndromes

Category / Non-billable header 5 subcodes

Block: Autoinflammatory syndromes (M04)

Excludes 2 (not included here)

  • Crohn's disease (K50.-)

Subcodes

Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.

Code Description Billable
M04..1 Periodic fever syndromes Yes
M04..2 Cryopyrin-associated periodic syndromes Yes
M04..3 VEXAS syndrome Yes
M04..8 Other autoinflammatory syndromes Yes
M04..9 Autoinflammatory syndrome, unspecified Yes

Last reviewed: September 2026