I27..83 Eisenmenger's syndrome

Billable

Includes

  • Eisenmenger's complex
  • (Irreversible) Eisenmenger's disease
  • Pulmonary hypertension with right to left shunt related to congenital heart disease

Code Also

  • underlying heart defect, if known, such as:
  • atrial septal defect (Q21.1-)
  • Eisenmenger's defect (Q21.8)
  • patent ductus arteriosus (Q25.0)
  • ventricular septal defect (Q21.0)

Last reviewed: September 2026