ICD-10-CM · Chapter 9

I27..0 Primary pulmonary hypertension

Billable

← I27 — Other pulmonary heart diseases Chapter 9: I00-I99

Includes

Heritable pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Primary group 1 pulmonary hypertension
Primary pulmonary arterial hypertension

Excludes 1 (cannot be coded together)

persistent pulmonary hypertension of newborn (P29.30)
pulmonary hypertension NOS (I27.20)
secondary pulmonary arterial hypertension (I27.21)
secondary pulmonary hypertension (I27.29)

Last reviewed: September 2026