D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

Category / Non-billable header 3 subcodes

Block: Other disorders of blood and blood-forming organs (D70-D77)

Excludes 1 (cannot be coded together)

  • (Abt-) Letterer-Siwe disease (C96.0)
  • eosinophilic granuloma (C96.6)
  • Hand-Schüller-Christian disease (C96.5)
  • histiocytic medullary reticulosis (C96.9)
  • histiocytic sarcoma (C96.A)
  • histiocytosis X, multifocal (C96.5)
  • histiocytosis X, unifocal (C96.6)
  • Langerhans-cell histiocytosis, multifocal (C96.5)
  • Langerhans-cell histiocytosis NOS (C96.6)
  • Langerhans-cell histiocytosis, unifocal (C96.6)
  • leukemic reticuloendotheliosis (C91.4-)
  • lipomelanotic reticulosis (I89.8)
  • malignant histiocytosis (C96.A)
  • malignant reticulosis (C86.0)
  • nonlipid reticuloendotheliosis (C96.0)

Subcodes

Each subcode links to a detail page with full clinical annotations.

Code Description Billable
D76..1 Hemophagocytic lymphohistiocytosis Yes
D76..2 Hemophagocytic syndrome, infection-associated Yes
D76..3 Other histiocytosis syndromes Yes

Last reviewed: September 2026