ICD-10-CM · Chapter 3 · D50-D89
D68 Other coagulation defects
Excludes 1 (cannot be coded together)
- abnormal coagulation profile NOS (R79.1)
Excludes 2 (not included here)
- coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
- coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Subcodes
Each subcode links to a detail page with full clinical annotations.
| Code | Description | Billable |
|---|---|---|
| D68..0 | Von Willebrand disease | No |
| D68..00 | Von Willebrand disease, unspecified | Yes |
| D68..01 | Von Willebrand disease, type 1 | Yes |
| D68..02 | Von Willebrand disease, type 2 | No |
| D68..020 | Von Willebrand disease, type 2A | Yes |
| D68..021 | Von Willebrand disease, type 2B | Yes |
| D68..022 | Von Willebrand disease, type 2M | Yes |
| D68..023 | Von Willebrand disease, type 2N | Yes |
| D68..029 | Von Willebrand disease, type 2, unspecified | Yes |
| D68..03 | Von Willebrand disease, type 3 | Yes |
| D68..04 | Acquired von Willebrand disease | Yes |
| D68..09 | Other von Willebrand disease | Yes |
| D68..1 | Hereditary factor XI deficiency | Yes |
| D68..2 | Hereditary deficiency of other clotting factors | Yes |
| D68..3 | Hemorrhagic disorder due to circulating anticoagulants | No |
| D68..31 | Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors | No |
| D68..311 | Acquired hemophilia | Yes |
| D68..312 | Antiphospholipid antibody with hemorrhagic disorder | Yes |
| D68..318 | Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors | Yes |
| D68..32 | Hemorrhagic disorder due to extrinsic circulating anticoagulants | Yes |
| D68..4 | Acquired coagulation factor deficiency | Yes |
| D68..5 | Primary thrombophilia | No |
| D68..51 | Activated protein C resistance | Yes |
| D68..52 | Prothrombin gene mutation | Yes |
| D68..59 | Other primary thrombophilia | Yes |
| D68..6 | Other thrombophilia | No |
| D68..61 | Antiphospholipid syndrome | Yes |
| D68..62 | Lupus anticoagulant syndrome | Yes |
| D68..69 | Other thrombophilia | Yes |
| D68..8 | Other specified coagulation defects | Yes |
| D68..9 | Coagulation defect, unspecified | Yes |
Last reviewed: September 2026