ICD-10-CM · Chapter 3
D56..0 Alpha thalassemia
Includes
- Alpha thalassemia major
- Hemoglobin H Constant Spring
- Hemoglobin H disease
- Hydrops fetalis due to alpha thalassemia
- Severe alpha thalassemia
- Triple gene defect alpha thalassemia
Excludes 1 (cannot be coded together)
- alpha thalassemia trait or minor (D56.3)
- asymptomatic alpha thalassemia (D56.3)
- hydrops fetalis due to isoimmunization (P56.0)
- hydrops fetalis not due to immune hemolysis (P83.2)
Use Additional Code
- code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
Last reviewed: September 2026