ICD-10-CM · Chapter 17 · Q00-QA1
Q80 Congenital ichthyosis
Excludes 1 (cannot be coded together)
- Refsum's disease (G60.1)
Subcodes
Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.
| Code | Description | Billable |
|---|---|---|
| Q80..0 | Ichthyosis vulgaris | Yes |
| Q80..1 | X-linked ichthyosis | Yes |
| Q80..2 | Lamellar ichthyosis | Yes |
| Q80..3 | Congenital bullous ichthyosiform erythroderma | Yes |
| Q80..4 | Harlequin fetus | Yes |
| Q80..8 | Other congenital ichthyosis | Yes |
| Q80..9 | Congenital ichthyosis, unspecified | Yes |
Last reviewed: September 2026