ICD-10-CM · Chapter 17 · Q00-QA1
Q75 Other congenital malformations of skull and face bones
Excludes 1 (cannot be coded together)
- congenital malformation of face NOS (Q18.-)
- congenital malformation syndromes classified to Q87.-
- dentofacial anomalies [including malocclusion] (M26.-)
- musculoskeletal deformities of head and face (Q67.0-Q67.4)
- skull defects associated with congenital anomalies of brain such as:
- anencephaly (Q00.0)
- encephalocele (Q01.-)
- hydrocephalus (Q03.-)
- microcephaly (Q02)
Subcodes
Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.
| Code | Description | Billable |
|---|---|---|
| Q75..0 | Craniosynostosis | No |
| Q75..00 | Craniosynostosis, unspecified | No |
| Q75..001 | Craniosynostosis, unspecified type, unilateral | Yes |
| Q75..002 | Craniosynostosis, unspecified type, bilateral | Yes |
| Q75..009 | Craniosynostosis, unspecified | Yes |
| Q75..01 | Sagittal craniosynostosis | Yes |
| Q75..02 | Coronal craniosynostosis | No |
| Q75..021 | Coronal craniosynostosis, unilateral | Yes |
| Q75..022 | Coronal craniosynostosis, bilateral | Yes |
| Q75..029 | Coronal craniosynostosis, unspecified | Yes |
| Q75..03 | Metopic craniosynostosis | Yes |
| Q75..04 | Lambdoid craniosynostosis | No |
| Q75..041 | Lambdoid craniosynostosis, unilateral | Yes |
| Q75..042 | Lambdoid craniosynostosis, bilateral | Yes |
| Q75..049 | Lambdoid craniosynostosis, unspecified | Yes |
| Q75..05 | Multi-suture craniosynostosis | No |
| Q75..051 | Cloverleaf skull | Yes |
| Q75..052 | Pansynostosis | Yes |
| Q75..058 | Other multi-suture craniosynostosis | Yes |
| Q75..08 | Other single-suture craniosynostosis | Yes |
| Q75..1 | Craniofacial dysostosis | Yes |
| Q75..2 | Hypertelorism | Yes |
| Q75..3 | Macrocephaly | Yes |
| Q75..4 | Mandibulofacial dysostosis | Yes |
| Q75..5 | Oculomandibular dysostosis | Yes |
| Q75..8 | Other specified congenital malformations of skull and face bones | Yes |
| Q75..9 | Congenital malformation of skull and face bones, unspecified | Yes |
Last reviewed: September 2026