Q61 Cystic kidney disease

Category / Non-billable header 13 subcodes

Block: Congenital malformations of the urinary system (Q60-Q64)

Excludes 1 (cannot be coded together)

  • acquired cyst of kidney (N28.1)
  • Potter's syndrome (Q60.6)

Subcodes

Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.

Code Description Billable
Q61..0 Congenital renal cyst No
Q61..00 Congenital renal cyst, unspecified Yes
Q61..01 Congenital single renal cyst Yes
Q61..02 Congenital multiple renal cysts Yes
Q61..1 Polycystic kidney, infantile type No
Q61..11 Cystic dilatation of collecting ducts Yes
Q61..19 Other polycystic kidney, infantile type Yes
Q61..2 Polycystic kidney, adult type Yes
Q61..3 Polycystic kidney, unspecified Yes
Q61..4 Renal dysplasia Yes
Q61..5 Medullary cystic kidney Yes
Q61..8 Other cystic kidney diseases Yes
Q61..9 Cystic kidney disease, unspecified Yes

Last reviewed: September 2026