ICD-10-CM · Chapter 17 · Q00-QA1
Q26 Congenital malformations of great veins
Subcodes
Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.
| Code | Description | Billable |
|---|---|---|
| Q26..0 | Congenital stenosis of vena cava | Yes |
| Q26..1 | Persistent left superior vena cava | Yes |
| Q26..2 | Total anomalous pulmonary venous connection | Yes |
| Q26..3 | Partial anomalous pulmonary venous connection | Yes |
| Q26..4 | Anomalous pulmonary venous connection, unspecified | Yes |
| Q26..5 | Anomalous portal venous connection | Yes |
| Q26..6 | Portal vein-hepatic artery fistula | Yes |
| Q26..8 | Other congenital malformations of great veins | Yes |
| Q26..9 | Congenital malformation of great vein, unspecified | Yes |
Last reviewed: September 2026