ICD-10-CM · Chapter 17 · Q00-QA1
Q01 Encephalocele
Includes
- Arnold-Chiari syndrome, type III
- encephalocystocele
- encephalomyelocele
- hydroencephalocele
- hydromeningocele, cranial
- meningocele, cerebral
- meningoencephalocele
Excludes 1 (cannot be coded together)
- Meckel-Gruber syndrome (Q61.9)
Subcodes
Subcodes are listed below for reference. Detail pages are not available for chapters 11–22.
| Code | Description | Billable |
|---|---|---|
| Q01..0 | Frontal encephalocele | Yes |
| Q01..1 | Nasofrontal encephalocele | Yes |
| Q01..2 | Occipital encephalocele | Yes |
| Q01..8 | Encephalocele of other sites | Yes |
| Q01..9 | Encephalocele, unspecified | Yes |
Last reviewed: September 2026