ICD-10-CM · Chapter 1 · A00-B99
A81 Atypical virus infections of central nervous system
Includes
- diseases of the central nervous system caused by prions
Use Additional Code
- code, if applicable, to identify:
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- mild neurocognitive disorder due to known physiological condition (F06.7-)
Subcodes
Each subcode links to a detail page with full clinical annotations.
| Code | Description | Billable |
|---|---|---|
| A81..0 | Creutzfeldt-Jakob disease | No |
| A81..00 | Creutzfeldt-Jakob disease, unspecified | Yes |
| A81..01 | Variant Creutzfeldt-Jakob disease | Yes |
| A81..09 | Other Creutzfeldt-Jakob disease | Yes |
| A81..1 | Subacute sclerosing panencephalitis | Yes |
| A81..2 | Progressive multifocal leukoencephalopathy | Yes |
| A81..8 | Other atypical virus infections of central nervous system | No |
| A81..81 | Kuru | Yes |
| A81..82 | Gerstmann-Straussler-Scheinker syndrome | Yes |
| A81..83 | Fatal familial insomnia | Yes |
| A81..89 | Other atypical virus infections of central nervous system | Yes |
| A81..9 | Atypical virus infection of central nervous system, unspecified | Yes |
Last reviewed: September 2026